نبذة مختصرة : Cilj: Prikazati rijedak klinički entitet, flail-arm sindrom, varijantu amiotrofične lateralne skleroze. Prikaz slučaja: Prikazujemo šezdesetosmogodišnjeg muškarca s atrofijom proksimalnih mišića gornjih ekstremiteta i ramenog pojasa. Miotatski refleksi u gornjim ekstremitetima nisu se izazivali, a u donjim ekstremitetima bili su pojačani. Plantarni je refleks obostrano bio fiziološki. Fascikulacije su bile vidljive u mišićima nadlaktica. Znakova slabosti bulbarnih mišića pacijent nije imao. Tijekom 27 mjeseci nakon nastupa simptoma njegovo je stanje bilo nepromijenjeno. Zaključak: Rezultati pretraga i klinička slika govore u prilog flailarm sindromu. ; Aim: To report a rare entity of flail-arm syndrome, a variant of amyotrophic lateral sclerosis. Case Report: We present a male patient at 68 years of age with proximal muscle atrophy of upper extremities and shoulders. Deep tendon reflexes in upper extremities were absent, while hyperactive in lower extremities. Plantar reflex was physiological on both sides. Fasciculations were visible in both arms. There were no signs of bulbar weakness. His condition was unchanged during 27 months after the onset of symptoms. Conclusion: The results of diagnostic procedures and clinical findings indicate the presence of flail-arm sindrome.
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