Management of urethral hemangiomas associated with Klippel-Trenaunay-Weber syndrome by endoscopic sclerotherapy.

Publisher: Blackwell Science Asia Country of Publication: Australia NLM ID: 9440237 Publication Model: Print Cited Medium: Print ISSN: 0919-8172 (Print) Linking ISSN: 09198172 NLM ISO Abbreviation: Int J Urol Subsets: MEDLINE

Publication: Carlton South, Vic. : Blackwell Science Asia
Original Publication: Tokyo ; New York : Churchill Livingstone, c1994-

Endoscopy*; Hemangioma/*complications ; Hemangioma/*therapy ; Klippel-Trenaunay-Weber Syndrome/*complications ; Sclerotherapy/*methods ; Urethral Neoplasms/*complications ; Urethral Neoplasms/*therapy; Adult ; Humans ; Male

Klippel-Trenaunay-Weber syndrome (KTS) is an unusual congenital anomaly characterized by cutaneous hemangiomas, varicosities and bony hypertrophy of the extremities. Herein the case is reported of a 24-year-old man with urethral bleeding from hemangiomas associated with KTS that were successfully managed by endoscopic sclerotherapy. A 23-G puncture needle was inserted into the bleeding vein to inject a 5% solution of monoethanolamine oleate (Oldamine), which is typically used for sclerotherapy of esophageal vasix. At a 4-month follow-up, the patient only had slightly bloodstained urethral discharge, and is doing well. This is the first case reporting endoscopic sclerotherapy for a KTS-associated urethral hemangioma.

Date Created: 20070725 Date Completed: 20071206 Latest Revision: 20070724

20231215

10.1111/j.1442-2042.2007.01571.x

17645615